Noncompaction cardiomyopathy: sinus node disease as an initial manifestation treated with bicameral pacemaker
Keywords:
Isolated Noncompaction of the Ventricular Myocardium, Pacemaker, Artificial, Sick Sinus SyndromeAbstract
Noncompaction cardiomyopathy is a congenital disease that results from myocardial compaction failure in embryonic life. In this process there is the persistence of deep trabeculations and recesses that communicate with the ventricular cavity, resulting in myocardial thickening in two distinct layers. The clinical aspect of this disease in both children and adults is very heterogeneous, ranging from absence of symptomatology to a triad including congestive heart failure, arrhythmias and systemic thromboembolism. However, symptomatic bradycardias are very rare. We report the case of a patient with sinus node disease as the initial manifestation of non-compaction cardiomyopathy.
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References
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13. Brignole M, Auricchio A, Baron-Esquivias G, et al. 2013 ESC Guidelines on cardiac pacing and cardiac resynchronization therapy: the Task Force on cardiac pacing and resynchronization therapy of the European Society of Cardiology (ESC). Developed in collaboration with the European Heart Rhythm Association (EHRA). Eur Heart J. 2013;34(29):2281-329.
2. Udeoji DU, Philip KJ, Morrissey RP, Phan A, Schwarz ER. Left ventricular noncompaction cardiomyopathy: updated review. Ther Adv Cardiovasc Dis. 2013;7(5):260-73. DOI: http://dx.doi. org/10.1177/1753944713504639
3. Celiker A, Ozkutlu S, Dilber E, Karagoz T. Rhythm abnormalities in children with isolated ventricular noncompaction. Pacing Clin Electrophysiol. 2005;28(11):1198-202. DOI: http://dx.doi.org/10.1111/ j.1540-8159.2005.09498.x
4. Ergul Y, Nisli K, Varkal MA, et al. Electrocardiographic findings at initial diagnosis in children with isolated left ventricular noncompaction. Ann Noninvasive Electrocardiol. 2011;16(2):184-91. DOI: http://dx.doi. org/10.1111/j.1542-474X.2011.00428.x
5. Sandhu R, Finkelhor RS, Gunawardena DR, Bahler RC. Prevalence and characteristics of left ventricular noncompaction in a community hospital cohort of patients with systolic dysfunction. Echocardiography. 2008;25(1):8-12.
6. Paterick TE, Gerber TC, Pradhan SR, Lindor NM, Tajik AJ. Left ventricular noncompaction cardiomyopathy: what do we know? Rev Cardiovasc Med. 2010;11(2):92-9.
7. Ritter M, Oechslin E, Sutsch G, Attenhofer C, Schneider J, Jenni R. Isolated noncompaction of the myocardium in adults. Mayo Clin Proc. 1997;72(1):26-31. PMID: 9005281 DOI: http://dx.doi.org/10.4065/72.1.26
8. Baysan O, Köz C, Uzun M, Yokuşoğlu M. An isolated case of left ventricular non-compaction with sick sinus syndrome. Anatol J Cardiol. 2008;8(2):175-6.
9. Ichida F, Hamamichi Y, Miyawaki T, et al. Clinical features of isolated noncompaction of the ventricular myocardium: long-term clinical course, hemodynamic properties, and genetic background. J Am Coll Cardiol. 1999;34(1):233-40. PMID: 10400016 DOI: http://dx.doi. org/10.1016/S0735-1097(99)00170-9
10. Milano A, Vermeer AM, Lodder EM, et al. HCN4 mutations in multiple families with bradycardia and left ventricular noncompaction cardiomyopathy. J Am Coll Cardiol. 2014;64(8):745-56. PMID: 25145517 DOI: http://dx.doi.org/10.1016/j.jacc.2014.05.045
11. Garcia-Pavia P, de la Pompa JL. Left ventricular noncompaction: a genetic cardiomyopathy looking for diagnostic criteria. J Am Coll Cardiol. 2014;64(19):1981-3. DOI: http://dx.doi.org/10.1016/j.jacc.2014.08.034
12. Martinelli Filho M, Zimerman LI, Lorga AM, Vasconcelos JTM, Rassi A Jr. Guidelines for Electronic Cardiac Implantable Devices of the Brazilian Society of Cardiology. Arq Bras Cardiol. 2007;89(6):e210-e238.
13. Brignole M, Auricchio A, Baron-Esquivias G, et al. 2013 ESC Guidelines on cardiac pacing and cardiac resynchronization therapy: the Task Force on cardiac pacing and resynchronization therapy of the European Society of Cardiology (ESC). Developed in collaboration with the European Heart Rhythm Association (EHRA). Eur Heart J. 2013;34(29):2281-329.
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Published
2018-04-01
How to Cite
Carlesso, V. B. ., Falsoni, M. ., Pinto de Oliveira, F. A. ., Maurício, V. A. de S. ., & Pachón Mateos, J. C. . (2018). Noncompaction cardiomyopathy: sinus node disease as an initial manifestation treated with bicameral pacemaker. JOURNAL OF CARDIAC ARRHYTHMIAS, 31(2), 73–75. Retrieved from https://jca.org.br/jca/article/view/72
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Section
Cardiac Pacing
