Noncompaction cardiomyopathy: sinus node disease as an initial manifestation treated with bicameral pacemaker

Authors

  • Vinícius Batista Carlesso Instituto Dante Pazzanese de Cardiologia
  • Manoela Falsoni Instituto Dante Pazzanese de Cardiologia
  • Fredric Assis Pinto de Oliveira Instituto Dante Pazzanese de Cardiologia
  • Vitória Adelaide de Sousa Maurício Instituto Dante Pazzanese de Cardiologia
  • Juan Carlos Pachón Mateos Instituto Dante Pazzanese de Cardiologia

Keywords:

Isolated Noncompaction of the Ventricular Myocardium, Pacemaker, Artificial, Sick Sinus Syndrome

Abstract

Noncompaction cardiomyopathy is a congenital disease that results from myocardial compaction failure in embryonic life. In this process there is the persistence of deep trabeculations and recesses that communicate with the ventricular cavity, resulting in myocardial thickening in two distinct layers. The clinical aspect of this disease in both children and adults is very heterogeneous, ranging from absence of symptomatology to a triad including congestive heart failure, arrhythmias and systemic thromboembolism. However, symptomatic bradycardias are very rare. We report the case of a patient with sinus node disease as the initial manifestation of non-compaction cardiomyopathy.

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Author Biographies

Vinícius Batista Carlesso, Instituto Dante Pazzanese de Cardiologia

Instituto Dante Pazzanese de Cardiologia, São Paulo, SP, Brasil.

Manoela Falsoni, Instituto Dante Pazzanese de Cardiologia

Instituto Dante Pazzanese de Cardiologia, São Paulo, SP, Brasil.

Fredric Assis Pinto de Oliveira, Instituto Dante Pazzanese de Cardiologia

Instituto Dante Pazzanese de Cardiologia, São Paulo, SP, Brasil.

Vitória Adelaide de Sousa Maurício, Instituto Dante Pazzanese de Cardiologia

Instituto Dante Pazzanese de Cardiologia, São Paulo, SP, Brasil.

Juan Carlos Pachón Mateos, Instituto Dante Pazzanese de Cardiologia

Instituto Dante Pazzanese de Cardiologia, São Paulo, SP, Brasil.

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Published

01-04-2018

How to Cite

Carlesso, V. B. ., Falsoni, M. ., Pinto de Oliveira, F. A. ., Maurício, V. A. de S. ., & Pachón Mateos, J. C. . (2018). Noncompaction cardiomyopathy: sinus node disease as an initial manifestation treated with bicameral pacemaker. JOURNAL OF CARDIAC ARRHYTHMIAS, 31(2), 73–75. Retrieved from https://jca.org.br/jca/article/view/72

Issue

Section

Cardiac Pacing