Sudden Death by Catecholaminergic Polymorphic Ventricular Tachycardia in Children

Morte Súbita por Taquicardia Ventricular Polimórfica Catecolaminérgica em Criança

Authors

  • Isabella João Milan
  • Fernando Mello Porto
  • Halim Cury Filho
  • Adão Bento de Lucena Neto
  • José Marco Nogueira Lima

Keywords:

Ventricular tachycardia, Cardiac sudden death, Tachycardia

Abstract

Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) is a severe cardiac arrhythmogenic hereditary illness, which affects children and young adults with a structurally healthy heart. Its prevalence is of one case in 10 thousand inhabitants. It is a potentially fatal illness, part of the differential diagnosis of
syncope in children. The present study has the purpose of relating the case of a child that, during the investigation of convulsive syncope, presented sudden death aborted due to CPVT and to describe the diagnosis difficulties of the case, comparing with data from the literature.

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References

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Published

19-10-2019

How to Cite

Milan, I. J. ., Porto, F. M. ., Cury Filho, H., Lucena Neto, A. B. de ., & Lima, J. M. N. . (2019). Sudden Death by Catecholaminergic Polymorphic Ventricular Tachycardia in Children: Morte Súbita por Taquicardia Ventricular Polimórfica Catecolaminérgica em Criança. JOURNAL OF CARDIAC ARRHYTHMIAS, 32(2), 118–121. Retrieved from https://jca.org.br/jca/article/view/31

Issue

Section

Cardiac Pacing

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