Sudden Death by Catecholaminergic Polymorphic Ventricular Tachycardia in Children

Morte Súbita por Taquicardia Ventricular Polimórfica Catecolaminérgica em Criança

  • Isabella João Milan
  • Fernando Mello Porto
  • Halim Cury Filho
  • Adão Bento de Lucena Neto
  • José Marco Nogueira Lima
Keywords: Ventricular tachycardia, Cardiac sudden death, Tachycardia

Abstract

Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) is a severe cardiac arrhythmogenic hereditary illness, which affects children and young adults with a structurally healthy heart. Its prevalence is of one case in 10 thousand inhabitants. It is a potentially fatal illness, part of the differential diagnosis of
syncope in children. The present study has the purpose of relating the case of a child that, during the investigation of convulsive syncope, presented sudden death aborted due to CPVT and to describe the diagnosis difficulties of the case, comparing with data from the literature.

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Published
19-10-2019
Section
Artificial Heart Stimulation