Congenital complete heart block

Characteristics of 34 patients submitted to definitive pacemaker implant or replacement

Authors

  • Iara Atié Malan
  • Andrea Rodrigues Viviani
  • Luiz Carlos Simões
  • Raizza Fernandes da Costa
  • Salem Dalla Bernardina Alcoforado Domingues
  • Marília Alcoforado Domingues
  • Alexandre Marques Abla
  • Gabriela de Mesquita Ferreira Bernardo

Keywords:

Pacemaker, Artificial, Atrioventricular Block, Heart Defects, Congenital

Abstract

Aims: Describe the characteristics of 34 patients under 18, with congenital complete heart block submitted for definitive pacemaker implant or replacement. Methods: We retrospectively analyzed patients who underwent pacemaker implant or replacement between January 2011 and May 2017 at a single center. The patients were divided into 2 groups (group I: implant and group II: replacement) and evaluated according to gender, age, congenital heart disease, implant indication, technique used, complications and mortality. Results: Thirty-four patients underwent definitive pacemaker implant or replacement, 47.1% of which were female. The median age at the time of implantation was 2 years and 6 months and median weight was 17.5 kg. Congenital heart disease was found in 52.9% of the patients. The indications for definitive pacemaker implant were heart rate lower than 70 bpm with heart disease or dysfunction (44.1%), heart rate less than 55 bpm without heart disease (26.5%), signs and  symptoms of low cardiac output (20.6%) and ventricular dysfunction (8.8%). The epicardial technique
was performed in 73.5% and the endocardial technique in 26.5% of the patients. A bicameral pacemaker was implanted in 53% and monocameral ventricular pacemaker in 47% of the patients. Complications were observed in 23.5%, with a mortality of 8.8% of the patients. Conclusions: The careful evaluation of the characteristics of these patients allows an adequate choice of the system and the implant technique. Just over half of the patients had congenital heart disease, the epicardial technique was the most performed, most received bicameral pacemaker, and complications and mortality were similar to the literature.

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Published

01-10-2018

How to Cite

Atié Malan, I., Rodrigues Viviani, A., Simões, L. C., Fernandes da Costa, R., Dalla Bernardina Alcoforado Domingues, S., Alcoforado Domingues, M., Marques Abla, A., & de Mesquita Ferreira Bernardo, G. (2018). Congenital complete heart block: Characteristics of 34 patients submitted to definitive pacemaker implant or replacement. JOURNAL OF CARDIAC ARRHYTHMIAS, 31(4), 160–166. Retrieved from https://jca.org.br/jca/article/view/100

Issue

Section

Cardiac Pacing

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